Perthes disease or Legg-Calve-Perthes disease as it is sometimes known, is a condition which develops in childhood and affects the hip joint. There are two parts to the hip joint; the ball or femoral head and the socket (acetabulum).
In cases of Perthes, the blood supply to the top of the thighbone (femur) around and underneath the ball part of the joint becomes disrupted. This means that the blood supply to the growth plate (epiphysis) is restricted, causing the bone to become soft and start to break up (necrosis).
It is not know why the blood supply to the hip becomes affected; it is not reported to be caused by physical injury or a problem with blood vessels in the rest of the body and there are no other childhood conditions which are known to be linked to Perthes.
In most cases, over time, the affected blood vessels begin to regrow, allowing new bone to be produced in the damaged area. Recovery may take several years as the bone around the femoral head reforms – in a similar, but more prolonged way, to the recovery of a bone following a fracture.
Symptoms and Presentation
Perthes is approximately 4 times as common in boys as girls and generally occurs between 4 and 8 years of age. Active children tend to be more affected. The first symptom is usually a painless limp, but symptoms can be very subtle, with a mild ache in the thigh or knee not being uncommon.
Medical agreement on the best way to treat Perthes has not yet been reached. Pain relief, such as analgesics, anti- inflammatory drugs and restricting high impact activity are commonly used to alleviate symptoms. Physiotherapy and or hydrotherapy and, potentially surgery to the femoral (thighbone) head are sometimes used. The final aims of such treatments are to help the child have a normally formed hip joint when the grow up.
Steps have also produced a guide to help parents and carers prepare themselves and their child for a hospital admission. Parents of children who are having surgery, followed by time spent in a spica cast, may find the Steps guide Hip Surgery and Spica Cast Care and the short film clips (below) about caring for an older child in a hip spica on the Steps You Tube page useful.
Steps have compiled a short fact sheet about Perthes its diagnosis and treatment.
Steps is currently working alongside The British Orthopaedic Surgery Surveillance (BOSS) Study, a nationwide study to report the incidence and outcomes in rare orthopaedic diseases. The initial focus of this long term, pioneering study is on Slipped Capital Femoral Epiphysis and Perthes’ Disease.